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Showing PLEKHA1TAPP1 is a alias.

PLEKHA1

Pleckstrin homology domain-containing family A member 1 · UniProt Q9HB21

Length
404 aa
Mass
45.6 kDa
Annotated
2026-06-10
16 papers in source corpus 11 papers cited in narrative 11 extracted findings
Cross-family judge vs UniProt: Affinage preferred faithfulness: 7/7 claims corpus-supported (100%)

Mechanistic narrative

Synthesis pass · prose summary of the discoveries below

PLEKHA1 (TAPP1) is a cytoplasmic adaptor protein that reads the lipid second messenger PtdIns(3,4)P2 through its C-terminal PH domain and acts as a negative regulator of PI3K-driven signaling (PMID:14516276, PMID:21204784). A 1.4 Å crystal structure defined the basis for its lipid selectivity: an alanine adjacent to the D-5 phosphate-binding site sterically excludes PtdIns(3,4,5)P3, restricting binding to PtdIns(3,4)P2, a specificity reversible by reciprocal Ala/Gly swaps with the related DAPP1 (PMID:11513726). Agonist- or receptor-stimulated, PI3K-dependent production of PtdIns(3,4)P2 drives translocation of PLEKHA1 from cytosol to the plasma membrane via this PH domain (PMID:11802782, PMID:12101241). At the membrane it functions as a scaffold, recruiting PDZ-domain partners including MUPP1, the tyrosine phosphatase PTPL1, and syntrophins through its C-terminal residues (PMID:11802782, PMID:14516276, PMID:15485858). Genetic disruption of PtdIns(3,4)P2 binding in TAPP1/TAPP2 double knock-in mice enhances Akt activation and whole-body insulin sensitivity, establishing the PtdIns(3,4)P2–PLEKHA1 interaction as a brake on the PI3K–Akt–insulin axis (PMID:21204784). Through its syntrophin interaction PLEKHA1 also modulates actin-based remodeling, controlling PDGF-induced dorsal circular ruffles (PMID:15485858), and a TAPP1 PH-domain biosensor reveals PtdIns(3,4)P2 enrichment at the plasma membrane and on intracellular organelles (PMID:14604433). In disease contexts, a PLEKHA1-TACC2 fusion drives oncogenic EphA2/AKT/MMP2 signaling and vascular mimicry in esophageal squamous-cell carcinoma (PMID:40615663).

Mechanistic history

Synthesis pass · year-by-year structured walk · 8 steps
  1. 2001 High

    Resolved why PLEKHA1 distinguishes PtdIns(3,4)P2 from PtdIns(3,4,5)P3, defining the structural code for its phosphoinositide selectivity.

    Evidence 1.4 Å crystal structure of the C-terminal PH domain with reciprocal Ala/Gly mutagenesis and lipid-binding assays

    PMID:11513726

    Open questions at the time
    • Does not address full-length protein conformation or in vivo membrane engagement
    • No structure of partner-bound complexes
  2. 2002 High

    Established that PtdIns(3,4)P2 binding by the PH domain drives PI3K-dependent membrane translocation and links PLEKHA1 to a PDZ-scaffold partner.

    Evidence Live-cell imaging, endogenous co-IP with MUPP1, PH-domain mutants, and wortmannin inhibition in Swiss 3T3/293 cells; BCR-stimulated recruitment in B-lymphoma cells

    PMID:11802782 PMID:12101241

    Open questions at the time
    • Functional consequence of MUPP1 recruitment at the membrane not defined
    • Accumulation in F-actin ruffles is correlative, not mechanistic
  3. 2003 High

    Identified PLEKHA1 as a negative regulator of Akt signaling that also tethers the phosphatase PTPL1, partially defining its adaptor output.

    Evidence Endogenous co-IP, in vitro lipid binding, localization imaging, and siRNA knockdown with IGF1-stimulated Akt readout in HEK-293 cells

    PMID:14516276

    Open questions at the time
    • Mechanism by which PLEKHA1 dampens Akt not resolved
    • PTPL1 substrate at the membrane not identified
  4. 2004 Medium

    Extended PtdIns(3,4)P2 signaling beyond the plasma membrane and mapped PLEKHA1 to a syntrophin-dependent actin-remodeling role.

    Evidence Immunoelectron microscopy with GST-TAPP1-PH probe and PTEN re-expression; yeast two-hybrid, PDZ-binding assays, and overexpression/rescue with syntrophins in NIH-3T3 cells

    PMID:14604433 PMID:15485858

    Open questions at the time
    • Role of intracellular PtdIns(3,4)P2 pools for PLEKHA1 unclear
    • How syntrophin binding mechanistically controls dorsal ruffle formation not defined
  5. 2011 High

    Provided in vivo genetic proof that PtdIns(3,4)P2 binding by TAPP1/TAPP2 restrains the PI3K–Akt–insulin axis.

    Evidence TAPP1 R211L / TAPP2 R218L knock-in mice with insulin clamp/glucose disposal assays and PtdIns(3,4,5)P3/Akt measurement in primary fibroblasts

    PMID:21204784

    Open questions at the time
    • Effector mechanism downstream of membrane-bound TAPP1 not pinned down
    • Tissue-specific contributions of each paralog not separated
  6. 2015 Medium

    Showed a PI3K-independent role: PLEKHA1 negatively regulates oligodendrocyte precursor differentiation via the Mek/Erk pathway.

    Evidence siRNA knockdown and overexpression in primary OPC cultures with myelin gene expression and Erk1/2 vs Akt phosphorylation readouts

    PMID:26242484

    Open questions at the time
    • Molecular link between PLEKHA1 and Erk activation not established
    • Single-lab finding without in vivo validation
  7. 2024 Medium

    Identified upstream translational control of PLEKHA1 by EIF4G2 and a pro-invasive role in hepatocellular carcinoma.

    Evidence RNA immunoprecipitation, IRES dual-luciferase reporter, polysome profiling, nascent synthesis assays, and combined siRNA depletion in HCC cells

    PMID:39213495

    Open questions at the time
    • How PLEKHA1 levels mechanistically drive migration/invasion not defined
    • IRES element within PLEKHA1 mRNA not mapped
  8. 2025 Medium

    Demonstrated that a PLEKHA1-TACC2 fusion is oncogenic, driving EphA2/AKT/MMP2 signaling and vascular mimicry.

    Evidence RNA-seq fusion identification, EphA2 ubiquitylation assay, transgenic mouse model with Trp53 deletion, and EphA2 inhibitor rescue in ESCC

    PMID:40615663

    Open questions at the time
    • Contribution of the PLEKHA1 portion versus TACC2 to fusion activity not dissected
    • Mechanism of reduced EphA2 ubiquitylation unresolved

Open questions

Synthesis pass · forward-looking unresolved questions
  • How PLEKHA1's PtdIns(3,4)P2-dependent scaffolding mechanistically connects to its diverse downstream outputs (Akt suppression, Erk regulation, actin/filopodial dynamics) across cell types remains unresolved.
  • No unifying effector mechanism linking membrane recruitment to specific signaling outputs
  • Filopodial PtdIns(3,4)P2–actin coupling shown only with biosensor in a preprint
  • PLEKHA1's direct catalytic or enzymatic partners at the membrane not fully enumerated

Mechanism profile

Synthesis pass · controlled-vocabulary classification · explore literature graph →
Molecular activity
GO:0008289 lipid binding 5 GO:0060090 molecular adaptor activity 3 GO:0098772 molecular function regulator activity 2
Localization
GO:0005886 plasma membrane 4 GO:0005829 cytosol 2 GO:0005856 cytoskeleton 2 GO:0005768 endosome 1 GO:0005783 endoplasmic reticulum 1
Pathway
R-HSA-162582 Signal Transduction 2 R-HSA-1430728 Metabolism 1

Evidence

Reading pass · 11 per-paper findings extracted from the source corpus
Year Finding Method Journal Conf PMIDs
2001 Crystal structure of the C-terminal PH domain of TAPP1 (PLEKHA1) at 1.4 Å resolution revealed the molecular basis for its specific binding to PtdIns(3,4)P2 but not PtdIns(3,4,5)P3. A key alanine residue adjacent to the D-5 inositol-phosphate-binding site (versus glycine in the related DAPP1) both sterically excludes PtdIns(3,4,5)P3 and induces a conformational change in neighboring residues. Mutagenesis confirmed this: the DAPP1 G→A mutation converted it to a TAPP1-like domain that only binds PtdIns(3,4)P2, while the TAPP1 A→G mutation permitted binding to PtdIns(3,4,5)P3. X-ray crystallography (1.4 Å) combined with site-directed mutagenesis and lipid-binding assays The Biochemical journal High 11513726
2002 TAPP1 (PLEKHA1) translocates from cytoplasm to plasma membrane upon agonist-stimulated PtdIns(3,4)P2 production in Swiss 3T3 and 293 cells. Translocation requires a functional PtdIns(3,4)P2-binding C-terminal PH domain and is blocked by the PI3K inhibitor wortmannin. Endogenously expressed TAPP1 co-immunoprecipitates with endogenous MUPP1 (a multi-PDZ-domain protein), and TAPP1/TAPP2 interact with the 10th and 13th PDZ domains of MUPP1 via their C-terminal amino acids, suggesting TAPP1 recruits MUPP1 to the plasma membrane in response to PtdIns(3,4)P2 elevation. Live-cell imaging, co-immunoprecipitation of endogenous proteins, PH-domain mutant analysis, wortmannin inhibition The Biochemical journal High 11802782
2002 TAPP1 and TAPP2 are recruited to the plasma membrane of human B-lymphoma cells (BJAB) upon B-cell antigen receptor (BCR) activation, with kinetics that are slow and sustained. The C-terminal PH domain alone is necessary and sufficient for BCR-induced membrane recruitment. Recruitment is abolished by PI3K blockade and constitutively driven by active PI3K. Membrane accumulation correlates with PtdIns(3,4)P2 (not PtdIns(3,4,5)P3) production. TAPP1 and TAPP2 preferentially accumulate in F-actin-rich membrane ruffles, implicating them in PI3K-driven cytoskeletal reorganization. Live-cell imaging, PI3K inhibitor/activator treatment, C-terminal PH domain truncation mutants, lipid production kinetics analysis Molecular and cellular biology High 12101241
2003 Endogenously expressed TAPP1 is constitutively associated with the protein-tyrosine phosphatase PTPL1 (FAP-1). PTPL1 binds TAPP1 and TAPP2 principally through its first PDZ domain, enabling PTPL1 to associate with PtdIns(3,4)P2 in vitro. The TAPP1–PTPL1 interaction maintains PTPL1 in the cytoplasm; upon hydrogen-peroxide-stimulated PtdIns(3,4)P2 production, the TAPP1–PTPL1 complex translocates to the plasma membrane. TAPP1 binding does not alter PTPL1 phosphatase activity itself. RNAi-mediated knockdown of TAPP1 in HEK-293 cells enhanced IGF1-stimulated Akt activation and phosphorylation, consistent with a negative-regulatory role. Co-immunoprecipitation of endogenous proteins, in vitro lipid-binding assay, cellular localization imaging, siRNA knockdown with Akt phosphorylation readout The Biochemical journal High 14516276
2004 Using GST-TAPP1-PH domain as a specific probe in on-section immunoelectron microscopy, PtdIns(3,4)P2 was detected not only at the plasma membrane but also on intracellular organelles including the endoplasmic reticulum and multivesicular endosomes after PDGF or hydrogen peroxide stimulation. Intracellular and plasma-membrane pools of PtdIns(3,4)P2 showed differential sensitivity to PTEN phosphatase, revealing compartmentally distinct signaling pools. Immunoelectron microscopy using GST-TAPP1-PH domain as a lipid probe, PTEN re-expression in PTEN-null cells The Biochemical journal Medium 14604433
2004 TAPP1 interacts with the PDZ domains of gamma1-, alpha1-, and beta2-syntrophin via its C-terminal amino acids; this interaction is required for correct subcellular localization of TAPP1. Both TAPP1 and syntrophins co-localize to PDGF-induced dorsal circular membrane ruffles in NIH-3T3 cells. Ectopic overexpression of TAPP1 blocks PDGF-induced dorsal circular ruffle formation, but co-expression of alpha1- or gamma1-syntrophin rescues this blockade, indicating that syntrophins regulate TAPP1-mediated actin cytoskeletal remodeling downstream of PI3K/PtdIns(3,4)P2 signaling. Yeast two-hybrid screen, biochemical PDZ domain binding assays, co-localization imaging, overexpression and rescue experiments in NIH-3T3 cells The Journal of biological chemistry High 15485858
2011 Knock-in mice homozygous for PtdIns(3,4)P2-binding-deficient mutations in both TAPP1 (R211L) and TAPP2 (R218L) are viable but display significantly enhanced Akt activation and improved whole-body insulin sensitivity with increased glucose disposal into muscle. Embryonic fibroblasts from double knock-in mice show enhanced IGF1-stimulated PtdIns(3,4,5)P3 production and Akt activity. This establishes that TAPP1/TAPP2 binding to PtdIns(3,4)P2 acts as a negative regulator of the PI3K–Akt–insulin signaling axis. Knock-in mouse genetics (R211L mutation), insulin clamp/glucose disposal assays, primary embryonic fibroblasts with PtdIns(3,4,5)P3 measurement and Akt phosphorylation The Biochemical journal High 21204784
2015 TAPP1 (PLEKHA1) is selectively expressed in differentiating oligodendrocyte precursor cells (OPCs). Knockdown of TAPP1 promotes OPC differentiation and myelin gene expression, while overexpression suppresses differentiation. TAPP1 inhibition alters Erk1/2 (but not Akt) phosphorylation, placing TAPP1 as a negative regulator of OPC differentiation specifically through the Mek/Erk pathway rather than the canonical PI3K/Akt axis. siRNA knockdown and overexpression in primary OPC cultures, myelin gene expression assays, western blot for Erk1/2 and Akt phosphorylation Neuroscience bulletin Medium 26242484
2024 EIF4G2 (a translation initiation factor) regulates PLEKHA1 protein expression via IRES-dependent translation in hepatocellular carcinoma (HCC). RNA immunoprecipitation showed EIF4G2 associates with PLEKHA1 mRNA, and dual-luciferase reporter assays confirmed IRES-dependent translational control. Polysome analysis and nascent protein synthesis assays validated EIF4G2 as the writer of this translational regulation. Combined depletion of EIF4G2 and PLEKHA1 synergistically inhibits HCC cell migration and invasion. RNA immunoprecipitation (RIP), dual-luciferase reporter assay, polysome profiling, nascent protein synthesis assay, siRNA knockdown Journal of proteome research Medium 39213495
2025 A PLEKHA1-TACC2 chromosomal fusion gene produces a fusion protein that upregulates the EphA2/AKT/MMP2 signaling pathway and promotes vascular mimicry formation in esophageal squamous-cell carcinoma (ESCC) by reducing ubiquitylation of EphA2. In vivo, PLEKHA1-TACC2 fusion combined with Trp53 deletion significantly increases tumor incidence in a transgenic mouse model, suppressible by EphA2 inhibitors. RNA sequencing identification of fusion transcript, in vitro and in vivo functional assays, ubiquitylation assay for EphA2, transgenic mouse model, pharmacological inhibition with EphA2 inhibitors Cell death and differentiation Medium 40615663
2025 Live imaging with a TAPP1 (PLEKHA1) 3xcPH domain probe in Xenopus laevis retinal ganglion cell filopodia showed that PtdIns(3,4)P2 accumulates specifically at filopodial tips. Quantitative cross-correlation and Granger causality analysis demonstrated that PI(3,4)P2 at filopodial tips both generates tip extension and responds to forward filopodial movement. Disruption of actin polymerization rapidly depleted tip PI(3,4)P2 prior to filopodial stalling, establishing a bidirectional relationship between PI(3,4)P2 and actin dynamics at filopodial tips. Live-cell TAPP1-3xcPH domain imaging, pharmacological PI3K perturbation, quantitative cross-correlation and Granger causality analysis, actin polymerization disruption bioRxivpreprint Medium bio_10.1101_2025.10.13.681625

Source papers

Stage 0 corpus · 16 papers · ranked by NIH iCite citations
Year Title Journal Citations PMID
2002 Evidence that the tandem-pleckstrin-homology-domain-containing protein TAPP1 interacts with Ptd(3,4)P2 and the multi-PDZ-domain-containing protein MUPP1 in vivo. The Biochemical journal 104 11802782
2002 TAPP1 and TAPP2 are targets of phosphatidylinositol 3-kinase signaling in B cells: sustained plasma membrane recruitment triggered by the B-cell antigen receptor. Molecular and cellular biology 98 12101241
2001 Crystal structure of the phosphatidylinositol 3,4-bisphosphate-binding pleckstrin homology (PH) domain of tandem PH-domain-containing protein 1 (TAPP1): molecular basis of lipid specificity. The Biochemical journal 76 11513726
2004 Detection of novel intracellular agonist responsive pools of phosphatidylinositol 3,4-bisphosphate using the TAPP1 pleckstrin homology domain in immunoelectron microscopy. The Biochemical journal 56 14604433
2004 The phosphoinositol 3,4-bisphosphate-binding protein TAPP1 interacts with syntrophins and regulates actin cytoskeletal organization. The Journal of biological chemistry 49 15485858
2003 Interaction of the protein tyrosine phosphatase PTPL1 with the PtdIns(3,4)P2-binding adaptor protein TAPP1. The Biochemical journal 45 14516276
2011 Role of TAPP1 and TAPP2 adaptor binding to PtdIns(3,4)P2 in regulating insulin sensitivity defined by knock-in analysis. The Biochemical journal 43 21204784
2007 PLEKHA1-LOC387715-HTRA1 polymorphisms and exudative age-related macular degeneration in the French population. Molecular vision 43 18079691
2005 Role of the adaptor proteins Bam32, TAPP1 and TAPP2 in lymphocyte activation. Immunology letters 34 15626471
2015 TAPP1 inhibits the differentiation of oligodendrocyte precursor cells via suppressing the Mek/Erk pathway. Neuroscience bulletin 14 26242484
2013 Cumulative association between age-related macular degeneration and less studied genetic variants in PLEKHA1/ARMS2/HTRA1: a meta and gene-cluster analysis. Molecular biology reports 10 24013816
2014 Study of Polymorphisms in CX3CR1, PLEKHA1 and VEGF genes as risk factors for age-related macular degeneration in Indian patients. Archives of medical research 9 25050486
2024 EIF4G2 Promotes Hepatocellular Carcinoma Progression via IRES-dependent PLEKHA1 Translation Regulation. Journal of proteome research 4 39213495
2024 Identification of JAZF1, KNOP1, and PLEKHA1 as causally associated genes and drug targets for Alzheimer's disease: a summary data-based Mendelian randomization study. Inflammopharmacology 2 39455528
2025 Aberrant formation of the neutrophil extracellular trap and the expression of the PLEKHA1 in systemic lupus erythematosus and ulcerative colitis. Molecular and cellular biochemistry 0 40379887
2025 The PLEKHA1-TACC2 fusion gene drives tumorigenesis via vascular mimicry formation in esophageal squamous-cell carcinoma. Cell death and differentiation 0 40615663

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