| 2004 |
Mutations in RDH12 encoding a photoreceptor cell retinol dehydrogenase cause childhood-onset severe retinal dystrophy. |
Nature genetics |
199 |
15258582 |
| 2004 |
Retinal dehydrogenase 12 (RDH12) mutations in leber congenital amaurosis. |
American journal of human genetics |
154 |
15322982 |
| 2006 |
Retinol dehydrogenase (RDH12) protects photoreceptors from light-induced degeneration in mice. |
The Journal of biological chemistry |
101 |
17032653 |
| 2005 |
Biochemical properties of purified human retinol dehydrogenase 12 (RDH12): catalytic efficiency toward retinoids and C9 aldehydes and effects of cellular retinol-binding protein type I (CRBPI) and cellular retinaldehyde-binding protein (CRALBP) on the oxidation and reduction of retinoids. |
Biochemistry |
98 |
15865448 |
| 2005 |
Retinal degeneration associated with RDH12 mutations results from decreased 11-cis retinal synthesis due to disruption of the visual cycle. |
Human molecular genetics |
86 |
16269441 |
| 2012 |
Reduction of all-trans-retinal in vertebrate rod photoreceptors requires the combined action of RDH8 and RDH12. |
The Journal of biological chemistry |
81 |
22621924 |
| 2007 |
RDH12 and RPE65, visual cycle genes causing leber congenital amaurosis, differ in disease expression. |
Investigative ophthalmology & visual science |
61 |
17197551 |
| 2006 |
Targeted disruption of the murine retinal dehydrogenase gene Rdh12 does not limit visual cycle function. |
Molecular and cellular biology |
57 |
17130236 |
| 2011 |
RDH12 retinopathy: novel mutations and phenotypic description. |
Molecular vision |
54 |
22065924 |
| 2018 |
RDH12 Mutations Cause a Severe Retinal Degeneration With Relatively Spared Rod Function. |
Investigative ophthalmology & visual science |
53 |
30372751 |
| 2008 |
Association of a novel mutation in the retinol dehydrogenase 12 (RDH12) gene with autosomal dominant retinitis pigmentosa. |
Archives of ophthalmology (Chicago, Ill. : 1960) |
51 |
18779497 |
| 2007 |
The phenotype of early-onset retinal degeneration in persons with RDH12 mutations. |
Investigative ophthalmology & visual science |
45 |
17389517 |
| 2007 |
Novel RDH12 mutations associated with Leber congenital amaurosis and cone-rod dystrophy: biochemical and clinical evaluations. |
Vision research |
41 |
17512964 |
| 2019 |
Detailed clinical characterisation, unique features and natural history of autosomal recessive RDH12-associated retinal degeneration. |
The British journal of ophthalmology |
36 |
30979730 |
| 2020 |
Expanding the phenotypic spectrum in RDH12-associated retinal disease. |
Cold Spring Harbor molecular case studies |
27 |
32014858 |
| 2008 |
Effect of lipid peroxidation products on the activity of human retinol dehydrogenase 12 (RDH12) and retinoid metabolism. |
Biochimica et biophysica acta |
27 |
18396173 |
| 2019 |
Retinol dehydrogenase 12 (RDH12): Role in vision, retinal disease and future perspectives. |
Experimental eye research |
26 |
31505163 |
| 2008 |
Complexity of phenotype-genotype correlations in Spanish patients with RDH12 mutations. |
Investigative ophthalmology & visual science |
25 |
19011012 |
| 2019 |
PHENOTYPIC VARIABILITY OF RECESSIVE RDH12-ASSOCIATED RETINAL DYSTROPHY. |
Retina (Philadelphia, Pa.) |
22 |
30134391 |
| 2014 |
Longitudinal clinical course of three Japanese patients with Leber congenital amaurosis/early-onset retinal dystrophy with RDH12 mutation. |
Documenta ophthalmologica. Advances in ophthalmology |
22 |
24752437 |
| 2021 |
Involvement of Oxidative and Endoplasmic Reticulum Stress in RDH12-Related Retinopathies. |
International journal of molecular sciences |
19 |
34445569 |
| 2019 |
Development of a Gene Therapy Vector for RDH12-Associated Retinal Dystrophy. |
Human gene therapy |
19 |
31237438 |
| 2022 |
RDH12 retinopathy: clinical features, biology, genetics and future directions. |
Ophthalmic genetics |
18 |
35491887 |
| 2007 |
RDH12, a retinol dehydrogenase causing Leber's congenital amaurosis, is also involved in steroid metabolism. |
The Journal of steroid biochemistry and molecular biology |
18 |
17512723 |
| 2020 |
Novel Heterozygous Deletion in Retinol Dehydrogenase 12 (RDH12) Causes Familial Autosomal Dominant Retinitis Pigmentosa. |
Frontiers in genetics |
16 |
32322264 |
| 2021 |
Novel disease-causing variant in RDH12 presenting with autosomal dominant retinitis pigmentosa. |
The British journal of ophthalmology |
14 |
34031043 |
| 2013 |
Exome sequencing identifies RDH12 compound heterozygous mutations in a family with severe retinitis pigmentosa. |
Gene |
14 |
23900199 |
| 2020 |
Macula-predominant retinopathy associated with biallelic variants in RDH12. |
Ophthalmic genetics |
13 |
32790509 |
| 2024 |
RDH12 allows cone photoreceptors to regenerate opsin visual pigments from a chromophore precursor to escape competition with rods. |
Current biology : CB |
11 |
38981477 |
| 2015 |
Exome Sequencing Identified a Recessive RDH12 Mutation in a Family with Severe Early-Onset Retinitis Pigmentosa. |
Journal of ophthalmology |
11 |
26124963 |
| 2009 |
Disease-associated variants of microsomal retinol dehydrogenase 12 (RDH12) are degraded at mutant-specific rates. |
FEBS letters |
10 |
20006610 |
| 2019 |
Natural History and Genotype-Phenotype Correlations in RDH12-Associated Retinal Degeneration. |
Advances in experimental medicine and biology |
9 |
31884613 |
| 2014 |
Genome-wide homozygosity mapping in families with leber congenital amaurosis identifies mutations in AIPL1 and RDH12 genes. |
DNA and cell biology |
9 |
25148430 |
| 2010 |
Novel RDH12 sequence variations in Leber congenital amaurosis. |
Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus |
8 |
20736127 |
| 2021 |
Generation of two human iPSC lines from patients with autosomal dominant retinitis pigmentosa (UCLi014-A) and autosomal recessive Leber congenital amaurosis (UCLi015-A), associated with RDH12 variants. |
Stem cell research |
7 |
34216980 |
| 2017 |
Phenotype-genotype correlation with Sanger sequencing identified retinol dehydrogenase 12 (RDH12) compound heterozygous variants in a Chinese family with Leber congenital amaurosis. |
Journal of Zhejiang University. Science. B |
7 |
28471114 |
| 2021 |
Gene Therapy for Rdh12-Associated Retinal Diseases Helps to Delay Retinal Degeneration and Vision Loss. |
Drug design, development and therapy |
6 |
34429587 |
| 2020 |
Report from a Workshop on Accelerating the Development of Treatments for Inherited Retinal Dystrophies Associated with Mutations in the RDH12 Gene. |
Translational vision science & technology |
5 |
32855876 |
| 2022 |
Associations Between Fundus Types and Clinical Manifestations in Patients with RDH12 Gene Mutations. |
Brain topography |
4 |
35006499 |
| 2022 |
Generation of a human induced pluripotent stem cell line (PUMCHi018-A) from an early-onset severe retinal dystrophy patient with RDH12 mutations. |
Stem cell research |
3 |
35016144 |
| 2025 |
Dominant RDH12-retinitis pigmentosa impairs photoreceptor development and implicates cone involvement in retinal organoids. |
Frontiers in cell and developmental biology |
2 |
40365019 |
| 2021 |
Simultaneous Identification of Both MFSD8 and RDH12 Pathogenic Variants in a Chinese Family Affected With Retinitis Pigmentosa. |
Frontiers in genetics |
2 |
34567070 |
| 2025 |
Generation of two iPSC lines (UGENTi003 and UGENTi004) from patients with intermediate rod-cone dystrophy carrying the c.[-123C>T;701G>A];[806_810del] variants in the RDH12 gene. |
Stem cell research |
1 |
40446715 |
| 2024 |
Generation of two hiPSC lines carrying compound heterozygous RDH12 mutations in a LCA patient. |
Stem cell research |
1 |
39142122 |
| 2023 |
Pseudocoloboma-like maculopathy with biallelic RDH12 missense mutations. |
Journal of medical genetics |
1 |
36690427 |
| 2022 |
New associations of serum β-carotene, lycopene, and zeaxanthin concentrations with NR1H3, APOB, RDH12, AND CYP genes. |
Food science & nutrition |
1 |
35282004 |
| 2026 |
Functional In Vitro Assessment of rAAV-Delivered Retinol Dehydrogenase 12 (RDH12) Activity. |
International journal of molecular sciences |
0 |
41683787 |
| 2026 |
WTAP mediated m6A methylation modulates retinal photoreceptor function via facilitating of REEP6, PDE6B and RDH12 translation. |
Science China. Life sciences |
0 |
41796262 |
| 2025 |
Genotype-phenotype relationship in RDH12 retinopathy: a perspective from a pediatric age group. |
Ophthalmic genetics |
0 |
40043730 |
| 2024 |
RDH12-associated retinal degeneration caused by a homozygous pathogenic variant of 146C>T and literature review. |
International journal of ophthalmology |
0 |
38371258 |
| 2024 |
Retinol dehydrogenase 12 (RDH12) knock out may cause hyperuricemia phenotype in mice. |
Biochemical and biophysical research communications |
0 |
38552555 |